Indian Journal of Paediatric Dermatology

CASE REPORT
Year
: 2019  |  Volume : 20  |  Issue : 2  |  Page : 160--162

A rare case of childhood mucous membrane pemphigoid involving both skin and mucosa


Monali Pattnaik1, Maitreyee Panda2, Mrutunjay Dash3, Chinmoy Raj2 
1 Department of DVL, SCB Medical College and Hospital, Cuttack, Odisha, India
2 Department of DVL, Institute of Medical Sciences and SUM Hospital, S ‘O' A University, Bhubaneswar, Odisha, India
3 Department of Paediatrics, Institute of Medical Sciences and SUM Hospital, S ‘O' A University, Bhubaneswar, Odisha, India

Correspondence Address:
Dr. Chinmoy Raj
Department of DVL, Institute of Medical Sciences and SUM Hospital, Kalinga Nagar, Bhubaneswar - 751 003, Odisha
India

Mucous membrane pemphigoid has been documented previously in only 19 patients under the age of 20 years. We report a 14-year-old female who had erosions of the oral, ocular, anal and genital mucosa, congestion, hoarseness of voice, dysphagia, and recurrent cough. Symblepharon formation in both eyes necessitated surgical correction. Biopsy of tissue from a solitary cutaneous lesion demonstrated a subepidermal bulla. Direct immunofluorescence showed the deposition of IgG in linear pattern along the dermoepidermal junction. Therapy was begun, consisting of prednisolone at 1 mg/kg/day, in combination with dapsone at 2 mg/kg/day. Azathioprine was added later for control of the disease. The patient showed good clinical response.


How to cite this article:
Pattnaik M, Panda M, Dash M, Raj C. A rare case of childhood mucous membrane pemphigoid involving both skin and mucosa.Indian J Paediatr Dermatol 2019;20:160-162


How to cite this URL:
Pattnaik M, Panda M, Dash M, Raj C. A rare case of childhood mucous membrane pemphigoid involving both skin and mucosa. Indian J Paediatr Dermatol [serial online] 2019 [cited 2019 Sep 18 ];20:160-162
Available from: http://www.ijpd.in/article.asp?issn=2319-7250;year=2019;volume=20;issue=2;spage=160;epage=162;aulast=Pattnaik;type=0