Indian Journal of Paediatric Dermatology

CASE REPORT
Year
: 2018  |  Volume : 19  |  Issue : 1  |  Page : 68--70

A rare case of neurocutaneous disorders of the newborn: Incontinentia pigmenti


Melek Aslan Kayiran1, Mehmet Salih Gürel2, Burçe Can Kuru2, Ilkin Zindancı2 
1 Department of Dermatology, Ümraniye Training and Research Hospital, Saglik Bilimleri University, Istanbul, Turkey
2 Department of Dermatology, Goztepe Research and Training Hospital, Istanbul Medeniyet University, Istanbul, Turkey

Correspondence Address:
Melek Aslan Kayiran
Fahrettin Kerim Gökay Cad. Ulus Apt. No: 62, D6 34724 Kadiköy, Istanbul
Turkey

Incontinentia Pigmenti (IP) is a rare X-linked dominant disorder which is mostly lethal for males. It effects hair, teeth, nails, eyes and central nervous system along with skin. A twelve day old female patient was referred to the dermatology departmant due to skin eruptions that began the day before. There was a widespread erythema and many papuls and vesicles were seen on the eryhematous skin in linear sequence. Spongiosis with eosinophilia and necrotic keratinocytes were seen on histopathologic examination. The patient was diagnosed with incontinentia pigmenti. Vesicles and bullous eruption are rarely seen in newborns. The physcians should not avoid histopathologic examination especially in females. Since incontinentia pigmenti is a rare but multisystemic disorder, early diagnosis is crucial.


How to cite this article:
Kayiran MA, Gürel MS, Kuru BC, Zindancı I. A rare case of neurocutaneous disorders of the newborn: Incontinentia pigmenti.Indian J Paediatr Dermatol 2018;19:68-70


How to cite this URL:
Kayiran MA, Gürel MS, Kuru BC, Zindancı I. A rare case of neurocutaneous disorders of the newborn: Incontinentia pigmenti. Indian J Paediatr Dermatol [serial online] 2018 [cited 2019 Sep 22 ];19:68-70
Available from: http://www.ijpd.in/article.asp?issn=2319-7250;year=2018;volume=19;issue=1;spage=68;epage=70;aulast=Kayiran;type=0